Un cas de nécrose médullaire compliquée d’embolie graisseuse chez un patient drépanocytaire (notice n° 83641)
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| fixed length control field | 02842cam a2200349 4500500 |
| 005 - DATE AND TIME OF LATEST TRANSACTION | |
| control field | 20250112000341.0 |
| 041 ## - LANGUAGE CODE | |
| Language code of text/sound track or separate title | fre |
| 042 ## - AUTHENTICATION CODE | |
| Authentication code | dc |
| 100 10 - MAIN ENTRY--PERSONAL NAME | |
| Personal name | Debus, Jérôme |
| Relator term | author |
| 245 00 - TITLE STATEMENT | |
| Title | Un cas de nécrose médullaire compliquée d’embolie graisseuse chez un patient drépanocytaire |
| 260 ## - PUBLICATION, DISTRIBUTION, ETC. | |
| Date of publication, distribution, etc. | 2019.<br/> |
| 500 ## - GENERAL NOTE | |
| General note | 43 |
| 520 ## - SUMMARY, ETC. | |
| Summary, etc. | Nous rapportons ici un cas de nécrose médullaire compliquée d’une embolie graisseuse cérébrale au décours d’une crise vaso-occlusive chez un patient drépanocytaire homozygote SS âgé de 23 ans. Suspectée devant l’apparition d’une bicytopénie sévère, la nécrose médullaire est confirmée par un myélogramme. Il s’agit du premier épisode grave présenté par ce patient. Ces complications rarement décrites de la drépanocytose sont potentiellement mortelles, mais d’évolution généralement favorable sous traitement symptomatique adapté. Dans le cas présenté ici, une allo-immunisation anti-érythrocytaire complexe a limité la transfusion et compliqué la prise en charge en raison des risques transfusionnels. La possibilité de nécrose médullaire dans le cadre de la drépanocytose doit être connue du biologiste afin d’orienter et de réaliser le diagnostic de cette grave complication. |
| 520 ## - SUMMARY, ETC. | |
| Summary, etc. | We report here a case of bone marrow necrosis and fat embolism syndrome in a 23-year-old sickle-cell disease (HbSS) patient. A brutal and severe bicytopenia conducted to suspect bone marrow necrosis, confirmed by bone marrow aspiration and analysis. This was the first life-threatening medical event for this patient. In the present case, a complex alloimmunization against blood group antigens complicated the treatment because of the risks associated with the transfusion strategy. These rare complications of sickle-cell disease may be fatal, but an efficient symptomatic treatment generally allows for recovery. Medical biologists should be aware of the danger of bone marrow necrosis in sickle-cell disease, so that they can help clinicians and accurately diagnose this serious complication. |
| 690 ## - LOCAL SUBJECT ADDED ENTRY--TOPICAL TERM (OCLC, RLIN) | |
| Topical term or geographic name as entry element | allo-immunisation complexe |
| 690 ## - LOCAL SUBJECT ADDED ENTRY--TOPICAL TERM (OCLC, RLIN) | |
| Topical term or geographic name as entry element | crise vaso-occlusive |
| 690 ## - LOCAL SUBJECT ADDED ENTRY--TOPICAL TERM (OCLC, RLIN) | |
| Topical term or geographic name as entry element | drépanocytose |
| 690 ## - LOCAL SUBJECT ADDED ENTRY--TOPICAL TERM (OCLC, RLIN) | |
| Topical term or geographic name as entry element | nécrose médullaire |
| 690 ## - LOCAL SUBJECT ADDED ENTRY--TOPICAL TERM (OCLC, RLIN) | |
| Topical term or geographic name as entry element | embolie graisseuse |
| 690 ## - LOCAL SUBJECT ADDED ENTRY--TOPICAL TERM (OCLC, RLIN) | |
| Topical term or geographic name as entry element | sickle-cell disease |
| 690 ## - LOCAL SUBJECT ADDED ENTRY--TOPICAL TERM (OCLC, RLIN) | |
| Topical term or geographic name as entry element | fat embolism |
| 690 ## - LOCAL SUBJECT ADDED ENTRY--TOPICAL TERM (OCLC, RLIN) | |
| Topical term or geographic name as entry element | bone marrow necrosis |
| 690 ## - LOCAL SUBJECT ADDED ENTRY--TOPICAL TERM (OCLC, RLIN) | |
| Topical term or geographic name as entry element | alloimmunization |
| 690 ## - LOCAL SUBJECT ADDED ENTRY--TOPICAL TERM (OCLC, RLIN) | |
| Topical term or geographic name as entry element | vaso-occlusive crisis |
| 700 10 - ADDED ENTRY--PERSONAL NAME | |
| Personal name | Dumont, Bénédicte |
| Relator term | author |
| 700 10 - ADDED ENTRY--PERSONAL NAME | |
| Personal name | Le Breton, Camille |
| Relator term | author |
| 700 10 - ADDED ENTRY--PERSONAL NAME | |
| Personal name | Emery, Malo |
| Relator term | author |
| 700 10 - ADDED ENTRY--PERSONAL NAME | |
| Personal name | Peynaud-Debayle, Edith |
| Relator term | author |
| 700 10 - ADDED ENTRY--PERSONAL NAME | |
| Personal name | Affo, Louis |
| Relator term | author |
| 786 0# - DATA SOURCE ENTRY | |
| Note | Annales de Biologie Clinique | 77 | 3 | 2019-05-01 | p. 318-322 | 0003-3898 |
| 856 41 - ELECTRONIC LOCATION AND ACCESS | |
| Uniform Resource Identifier | <a href="https://shs.cairn.info/revue-annales-de-biologie-clinique-2019-3-page-318?lang=fr">https://shs.cairn.info/revue-annales-de-biologie-clinique-2019-3-page-318?lang=fr</a> |
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