Felk, Rime

Immunoglobin G4-related disease as a rare cause of polycythemia: A case report - 2023.


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Immunoglobulin G4 (IgG4) disease is a recently described condition with a growing list of associated disorders. The most common manifestations are pancreatitis, infiltration of the salivary or lacrimal glands (Mikulicz syndrome), and retroperitoneal fibrosis. We present the case of a patient in whom polycythemia was secondary to IgG4 disease. Through a review of the literature, we discuss the clinical, radiological, and therapeutic aspects of this rare condition.