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041 _afre
042 _adc
100 1 0 _aSchieber, Hélène
_eauthor
700 1 0 _a Hadj-Rabia, Smail
_eauthor
700 1 0 _a Giuseppi, Agnès
_eauthor
700 1 0 _a Iacobelli, Silvia
_eauthor
700 1 0 _a Quetin, Frédérique
_eauthor
700 1 0 _a Kermorvant-Duchemin, Elsa
_eauthor
700 1 0 _a Bodemer, Christine
_eauthor
700 1 0 _a Lapillonne, Alexandre
_eauthor
245 0 0 _aHydroelectrolytic and nutritional needs of infants with epidermolysis bullosa during the first month of life
260 _c2024.
500 _a3
520 _aBackgroundDehydration and malnutrition are common in infants with severe epidermolysis bullosa (EB), but their nutritional needs have been poorly studied.ObjectivesThe principal aim was to assess the nutritional status, fluid and electrolyte balance, and nutritional intake of newborns with EB during the first month of life and estimate their needs during this period.Materials & MethodsThis was a retrospective study over an eight-year period. Inclusion criteria were neonates with confirmed EB admitted to our neonatal referral unit during the first month of life. Exclusion criteria were hospitalisations ResultsTwenty-seven patients with EB (mean [min-max] gestational age = 39 weeks [33; 41]; birth weight = 2986 g [1982; 4150]), were included. Four patients (15%) had hyponatraemia ConclusionThe rate of sodium deficit in neonates with EB is high and related to the significance of skin exudate. The administration of nutrient intake greater than that recommended helps to prevent acquired growth restriction. We propose recommendations for nutritional intake and monitoring in neonates with EB in the first month of life.
690 _aepidermolysis bullosa
690 _ahyponatremia
690 _ahydro-electrolytic disorders
690 _aprotein intake
690 _aneonates
690 _anutritional intake
786 0 _nEuropean Journal of Dermatology | 34 | 4 | 2024-07-09 | p. 384-391 | 1167-1122
856 4 1 _uhttps://shs.cairn.info/revue-european-journal-of-dermatology-2024-4-page-384?lang=en&redirect-ssocas=7080
999 _c604614
_d604614